PERINATOLOGIYA I PEDIATRIYA.2014.1(57):74-77; doi 10.15574/PP.2014.57.74

  
Quality of life features in children with primary immunodeficiencies 

Bondarenko A. V. 
Shupyk National Academy of Postgraduate Education, Kyiv, Ukraine

Primary immunodeficiencies (PID) are congenital disorders of the immune system which require lifelong medical support. So the main goal of treatment is to improve the quality of life. The article presents the results of a survey of quality of life in 52 PID patients in comparison with 76 healthy children. Quality of life in patients with PID in all categories is significantly worse compared with healthy controls. The worst quality of life is observed in phagocytic defects and in chronic mucocutaneous candidiasis patients. The main factors reflecting the quality of life in PID patients are regular and continuous treatment together with treatment compliance.

Key words: primary immunodeficiency, health1related quality of life, children.

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