Paediatric Surgery (Ukraine). 2025. 1(86): 110-120. doi: 10.15574/PS.2025.1(86).110120
Sliepov O. K.¹, Perederii O. V.¹, Znak K. L.¹, Grebinichenko G. O.², Zadorozhnya T. D.², Bondarenko Yu. M.², Hladishko O. P.^2
1Center for neonatal surgery for malformations and their rehabilitation of SI «Ukrainian Center of Maternity and Childhood of the of the NAMS of Ukraine», Kyiv
²SI «Ukrainian Center of Maternity and Childhood of the NAMS of Ukraine», Kyiv

For citation: Sliepov OK, Perederii OV, Znak KL, Grebinichenko GO, Zadorozhnya TD, Bondarenko YuM, Hladishko OP. (2025). Perinatal diagnosis and surgical correction of intralobar sequestration associated with cystic-adenomatous malformation of right lung, in a newborn. Paediatric Surgery (Ukraine). 1(86): 110-120. doi: 10.15574/PS.2025.1(86).110120.
Article received: Oct 17, 2024. Accepted for publication: Mar 18, 2025.

Aim – to analyze and describe the experience of surgical treatment of symptomatic intralobar pulmonary sequestration associated with cystic-adenomatous malformation of the lower lobe of the right lung in a newborn child based on a clinical case.
Clinical case. A unique clinical case of treatment of symptomatic intralobar pulmonary sequestration associated with cystic-adenomatous malformation of the lower lobe of the right lung in a newborn child is presented. Features of perinatal support, preoperative preparation, and surgical intervention are described, which are important elements of optimizing the treatment of children with this life-threatening pathology.
Conclusions. A scientifically based, differentiated approach is needed in the diagnosis and treatment of pulmonary sequestration, which includes: early (up to 22 weeks of gestation) complex prenatal diagnosis, to choose a rational pregnancy management tactic; examination of the fetus, with an assessment of its general condition, the dynamics of the pathological process during gestation; delivery of a pregnant woman according to the obstetric situation; postnatal diagnosis; preoperative preparation and surgical treatment in the conditions of a multifunctional perinatal center. Ultrasound with Doppler mapping is the leading method of prenatal diagnosis of pulmonary sequestration for choosing rational tactics of pregnancy management, as well as fetal examination. With symptomatic intralobar pulmonary sequestration and associated cystic-adenomatous malformation, within one lobe of the lung, it is advisable to perform a simultaneous operation: correction of both lung defects by lobectomy in the neonatal period, which prevents possible complications and gives good functional results.
The research was carried out in accordance with the principles of the Declaration of Helsinki. Informed consent of the woman was obtained for the research.
The authors declare no conflict of interest.
Keywords: pulmonary intralobar sequestration, cystic adenomatous malformation, prenatal diagnosis, perinatal support, fetal examination, newborn child.

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