PERINATOLOGIYA I PEDIATRIYA.2015.4(64):40-45; doi 10.15574/PP.2015.64.40 
 

Late diagnosed congenital diaphragmatic hernia of Morgagni: diagnostics and surgical correction in children 
 

Slepov O. K., Kurinnyi S. I., Golopapa G. V., Gladyshko O. P.

SE «Insitute of Pediatrics, Obstetrics, Gynecology of NAMS of Ukraine», Kyiv 
 

Purpose — research frequency, clinical and anatomical peculiarities of Morgagni hernias, develop diagnostic work-up and methods of surgical treatment. 
 

Patients and methods. In the department of surgical correction of congenital anomalies of the SE «IPOG NAMSU» 185 patients with different anatomical types of diaphragmatic hernia were treated during last 28 years. 6 children had late diagnosed Morgagni hernias. We used clinical, radiological, sonographic and statistical research method. 
 

Results. Clinical signs of Morgagni hernias include: inability of weight gain (n=4), dyspnoe (n=3), recurrent broncho-pulmonary illnesses (n=3), non-specific functional dysfunctions of alimentary canal (constipation — 2, pain in abdomen — 1). Work-up included: plain chest and abdominal X_ray (n=6), passage (n=3), contrast enema (n=2), ultrasonography (n=6), CT (n=2). All patients (n=6) were treated surgically. We used laparotomy (n=5) and thoracotomy (n=1) incisions. Operative correction consisted of hernia sac excision, and plastics using local tissues. Hernia organs were: transverse colon (n=3), liver (n=4), big omentum (n=1). There were no intraoperative and postoperative complications. 
 

Conclusions. Late diagnosed congenital hernias of Morgagni are very rare congenital anomalies that compose 3.2% of all diaphragmatic hernias. Recurrent bronco-pulmonary illnesses and inability of weight gain are more frequent signs of the illness. Developed work-up includes: plain chest and abdominal X-ray, contrast study (passage and enema), ultrasonography and CT. Treatment is surgical through laparotomy incision, hernia sac excision and plastics using local tissues. 
 

Key words: Late diagnosed congenital diaphragmatic hernia of Morgagni, diagnostics, surgical treatment, children. 
 

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