SOVREMENNAYA PEDIATRIYA.2016.3(75):126-128; doi10.15574/SP.2016.75.126 

Esophageal achalasia in children — clinical case and literature review 

Ivantsiv-Griga I. S.

Danylo Halytsky Lviv National Medical University, Ukraine 

Introduction. Esophageal achalasia is a primary disorder of the motor function characterized by the increased pressure in the lower esophageal sphincter, impairment of its reflex relaxation and inhibited peristalsis of the esophagus which, in turn, leads to functional obstruction of the distal section of the esophagus.

Goal. Improvement of early diagnosis and treatment outcomes of esophageal achalasia in children.

Materials and methods. Clinical observation, laboratory and instrumental examination of a 10 year old child with esophageal achalasia.

Results. The results of clinical data and laboratory and instrumental examination methods were analized and the diagnosis of esophageal achalasia in a 10 year old male was confirmed.

Conclusions. The described clinical case provided an opportunity for a thorough analysis of the clinical aspects of diagnosis and treatment of the given pathology. Esophageal achalasia is a rare pathology in children and has an atypical clinical manifestation; therefore, primary care physicians should study this disorder in detail and make a great effort to diagnose it in a timely manner.

Key words: achalasia cardiae, children, dysphagia, regurgitation.

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