PERINATOLOGIYA I PEDIATRIYA. 2016.3(67):10-14; doi 10.15574/PP.2016.67.10 
 

A Case of Еndovascular Repair of Mid-Aortic Syndrome Diagnosed During Pregnancy 

Cherpak B., Davydova I., Ditkivskyy I., Yaschuk N., Batsak B., Lazoryshynets V.

SI «National Institute for Cardiovascular Surgery named after M.M. Amosov», Kiev, Ukraine 
 

The mid-aortic syndrome is a clinical condition generated by segmental narrowing of the abdominal or descending thoracic aorta. It might be either a congenital abnormality in the development of aorta or one of several acquired conditions such as infection, obliterative panarteritis, neurofibromatosis, retroperitoneal fibrosis, fibromuscular dysplasia, mucopolysaccharidosis and Takayasu's arteritis. We are presenting a case of 17-years old female with life threatening hypertension during the onset of pregnancy and unrecognized before the gestation middle aortic syndrome. Because of rarity of this syndrome, only ridiculous evidence exists with regard to the treatment. Single cases of surgery and interventional treatment with stent-graft placement have been reported, as well as good outcomes with only medical management. Unfortunately, the arterial hypertension in our patient was resistant on 3-drug antihypertensive regimen. She has successful endovascular mid-aortic syndrome repaired with CP covered stent on the 24-th week of pregnancy. The blood pressure decreased from 220/110 mmHg to 140/90 mmHg after the procedure. 3 months later the patient experienced the spontaneous vaginal delivery and gave birth to a healthy male newborn.

Key words: mid-aortic syndrome, pregnancy, endovascular stent graft placement.

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