PERINATOLOGIYA I PEDIATRIYA.2015.2(62):16-21;doi10.15574/PP.2015.62.16

Congenital anomalies of the aortic arch: perinatal management

Lukianova I. S., Truba Y. P., Medvedenko G. F., Zhadan O. D., Ivanova L.A.

SI «Institute of Pediatrics, Gynecology and Obstetrics NAMN of Ukraine», Kyiv, Ukraine

SU «N.M. Amosov National Institute of Cardiovascular Surgery NAMS of Ukraine», Kiev, Ukraine

Purpose — according to the literature data and analysis of the own results to make recommendations for improvement of the detection of abnormalities of the aorta with the aim of timely cardiac care.

Patients and methods. For the period of 2011-2014 at SI «IPOG NAMSU» and SI «NICS NAMSU» were observed 222 pregnant women prenatally and 169 infants with hemodynamically significant CHD postnatally, including 39 children with the pathology of the aortic arch. The leading role in the diagnosis of congenital heart disease and providing timely cardiac care to the newborn belonged to fetal echocardiography (ECHO). All the children were consulted at SI «NICS NAMSU» in order to clarify the diagnosis and determine the further management. In all cases of isolated critical coarctation of the aorta or aortic arch hypoplasia, newborns in the first days or even hours of life were hospitalized in the department of congenital heart defects.

Results. In 18 (46.2%) neonates hypoplasia of the aortic arch was part of the hypoplastic left-heart syndrome. Conclusion. After diagnosis or suspicion of pathology of the aortic arch in the fetus (alone or in combination with other anomalies of the heart) the compulsory notification of neonatologists facilitates timely diagnosis and the providing, if necessary, cardiac surgery before the development of complications.

Key words: fetus, neonate, anomaly of the aortic arch, prenatal echocardiography, cardiac surgery.