• Rare anorectal malformation – a congenital pouch colon in neonates: literature review and own observation

Rare anorectal malformation – a congenital pouch colon in neonates: literature review and own observation

PAEDIATRIC SURGERY.UKRAINE.2018.2(59):72-76; DOI 10.15574/PS.2018.59.72

Fofanov O. D., Fofanov V. O., Banasevych V. V.
Ivano-Frankivsk National Medical University, Ukraine
CI Ivano-Frankivsk Oblast Children's Clinical Hospital, Ukraine

The article presents literary data on distribution, morphological signs, clinics, diagnostics and treatment of rare defects (especially in the European countries) – congenital pouch colon (CPC) in association with anorectal agenesis in newborns. The actual clinical observation of this combined defect in a newborn girl is also given. The authors concluded that the pathognomonic feature of CPC is the presence of a large gas bubble of the colon, which occupies more than 50% of the abdominal width in a child with anorectal agenesis on the plain abdominal X-ray or invertogram, and ultrasound signs of cystic enlargement of the colon. Tactics of surgical correction and prognosis are largely dependent upon the type of CPC and of associated anorectal malformation.
Key words: congenital pouch colon, anorectal malformations, newborns.

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