• Pregnancy and delivery in patients with Marfan syndrome (Сase study)

Pregnancy and delivery in patients with Marfan syndrome (Сase study)

HEALTH OF WOMAN. 2016.6(112):62–65 

Pregnancy and delivery in patients with Marfan syndrome (Сase study) 

Golyanovskyy O. V., Rubinshtein A. M., Strashevych K. V.

Shupyk National Medical Academy of Postgraduate Education, Kiev 

The article is devoted to the problem of pregnancy, delivery and the postpartum period in patients with Marfan syndrome – the system genetically determined pathology of the connective tissue. This disease is often accompanied by disorders of the vascular wall with the formation and subsequent stratification of aneurysms. Today the basic diagnostic method for vascular aneurysms remains echocardiography, which allows estimating the degree of vascular dilation and determining the tactics for such patients.

The article presents the clinical case of pregnancy, delivery and the postpartum period management in patient with Marfan syndrome, portal hypertension, subhepatic form, compensated by the essential porto-caval anastomosis, aneurysm of the vena cava inferior.

Key words: Marfan syndrome in pregnancy, abdominal aortic aneurysm, portal hypertension syndrome.


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