• Diagnostics of anomalous origin of the left coronary artery arising from pulmonary artery. 
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Diagnostics of anomalous origin of the left coronary artery arising from pulmonary artery. 

 

SOVREMENNAYA PEDIATRIYA.2014.2(58):76-78; doi 10.15574/SP.2014.58.76 
 

Diagnostics of anomalous origin of the left coronary artery arising from pulmonary artery. 
 

Sekelyk R. I., Ostras O. V., Artemenko E. А., Pavlova A. A., Kurkevich A. K.

Ukrainian Children’s Cardiac Center, Kiev, Ukraine 

Objective. The aim of this work was to study the efficiency of diagnostics of the anomalous origin of the left coronary artery from a pulmonary artery (ALCAPA) in Ukraine and the diagnostic algorithm for this cardiac anomaly introduced by us. 
 

Patients and methods. Thirty seven patients with ALCAPA were operated on in Ukrainian Children`s Cardiac Center (UCCC) from 2003 to 2013. The patient's diagnoses by the time of direction in our center from the different regions of Ukraine were analyzed. The anamnesis and hospital charts were analyzed, aiming to recognize the most typical diagnostic signs of ALCAPA. 
 

Results. Research showed that a correct diagnosis has been made only in 7(18,9%) patients. 27(79,4%) patients were misdiagnosed. 7(25,9%) patients were misdiagnosed with dilated cardiomyopathy, 5(18,5%) patients — with myocarditis, 4(14,8%) patients — with congenital mitral insufficiency, 4(14,8%) patients — with ventricular septal defect and 3(11,1) patients — with coarctation of aorta. This diagnoses proved to be the commonest ones in misdiagnosing ALCAPA.

Conclusions. Diagnostics of ALCAPA is ineffective in Ukraine. Increasing number of patients with ALCAPA correctly diagnosed during the last years proves the efficiency of the diagnostic algorithm introduced by us. 
 

Key words: diagnostics of the anomalous origin, left coronary artery, pulmonary artery. 
 

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