• Clinical manifestations of vascular disorders in children with undifferentiated connective tissue dysplasia who are living in the radiation monitoring area
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Clinical manifestations of vascular disorders in children with undifferentiated connective tissue dysplasia who are living in the radiation monitoring area

PERINATOLOGIYA I PEDIATRIYA. 2016.4(68):81-85; doi 10.15574/PP.2016.68.81 
Clinical manifestations of vascular disorders in children with undifferentiated connective tissue dysplasia who are living in the radiation monitoring area
Oshlyanska O. A., Hyndych Yu. Yu., Belinhio T. O., Studenikina O. M., Gryshchenko K. V., Tsvyet L. A.
SI «Institute of Pediatrics, Obstetrics and Gynecology of NAMS of Ukraine», Kyiv
SI «National Research Center for Radiation Medicine NAMS of Ukraine», Kyiv

Purpose — to determine the characteristics of the clinical manifestations of heart disease and blood vessels in children with heptrmobility syndrome living in areas of radiation monitoring.
Patients and methods. A retrospective analysis of data of clinical examinations carried out on the basis of advice of child health clinics SI «Institute of Pediatrics, Obstetrics and Gynecology of NAMS of Ukraine» further conducted a retrospective analysis of 101 of the histories Clinics Hospital of SI «National Research Centre for Radiation Medicine of NAMS of Ukraine», analyzed the patients' complaints, the description of the objective status and instrumental data study: ECG, ultrasound of the heart, rheoencephalography. These children survey of radiation control zones were compared with historical data from other surveys of children living regions.
Results. The analyzed data indicate that children from radiation control zone with heptrmobility syndrome manifestations were more frequent than in non-clean areas. Among the surveyed children with cardiovascular pathology heptrmobility syndrome recorded more frequently than children without signs heptrmobility syndrome. Complaints showing functional disorders with the disfunction of cardiovascular system, hearts microanomalies development by ultrasound of the heart, functional disorders of the vascular function according rheoencephalography children from radiation-controlled areas and manifestations heptrmobility syndrome detected more frequently than in patients from ecologically clean areas.
Conclusions. The survey revealed a high frequency of registration signs of connective tissue dysplasia, which is more common in children with a history of radiation burdened. A greater frequency of functional disorders of the blood vessels and heart microanomalies children with heptrmobility syndrome and radiation burdened history. Vascular disorders in heptrmobility syndrome require further more in-depth examination.
Key words: vascular disorders in children, undifferentiated connective tissue dysplasia, the accident at Chernobyl, children, increased radiation control zone.


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