• Clinical follow-up of a child with Williams—Campbell syndrome in the context of modern methods of diagnostics and treatment

Clinical follow-up of a child with Williams—Campbell syndrome in the context of modern methods of diagnostics and treatment

SOVREMENNAYA PEDIATRIYA.2018.6(94):53-58; doi 10.15574/SP.2018.94.53

Gonchar M. A., Logvinova O. L., Pushkar E. M., Pomazunovskaya E. P., Telnova L. G., Petrenko E. K.
Kharkiv National Medical University, Ukraine
CHPI «Regional Children's Clinical Hospital», Kharkiv, Ukraine

The article presents a clinical long$term follow$up of a young child with the bronchial obstruction syndrome, associated with expectoration of purulent sputum (up to 10 ml for one$time aspiration, ~ 140-200 mL per day). During the differential diagnostics, the congenital anomaly of the tracheobronchial tree was revealed, which turned out to be Williams-Campbell syndrome. Comparison of the malformation combination and course features of Williams-Campbell syndrome, identified in the child, with the literature data, as well as recommendations for monitoring and management of the patients with cystic bronchiectasis are described in the article.

Key words: Williams-Campbell syndrome, malformations, anomalies, bronchi, children, diagnostics, treatment.


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Article received: Mar 02, 2018. Accepted for publication: Sep 30, 2018.