• The clinical case of the child with cystic fibrosis and multiple organ failure syndrome development

The clinical case of the child with cystic fibrosis and multiple organ failure syndrome development

SOVREMENNAYA PEDIATRIYA.2017.5(85):132-136; doi 10.15574/SP.2017.85.132

Drobova N. M., Yanovska K. O., Pasichnyk O. V., Klymenko V. A., Piontkovska O. V., Bevz S. I., Sindeeva N. T.
Kharkiv National Medical University, Ukraine
Kharkiv Regional Clinical Children's Hospital №1, Ukraine

The clinical case of the child with cystic fibrosis and severe delF508 CFTR mutation is described in the article. This patient died from multiorgan failure syndrome
at 17 years old.
Key words: children, cystic fibrosis, liver cirrhosis, multiorgan failure syndrome.


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