• The case of Kazabah—Merritt syndrome in a child

The case of Kazabah—Merritt syndrome in a child

SOVREMENNAYA PEDIATRIYA.2018.7(95):47-50; doi 10.15574/SP.2018.95.47

Makieieva N., Odinets Yu., Poddubnaya I.
Kharkiv National Medical University, Ukraine
Communal nonprofit enterprise «Municipal Clinical Children's Hospital No.16» of the Kharkiv City Council, Ukraine

Kazabah—Merritt syndrome is usually combined with a large or even «giant» hemangioma and is accompanied by high mortality (37%). The most frequent localization of hemangiomas is the neck, face, head, trunk, less often internal organs, mainly the liver and brain. Unequivocally effective therapy of this disease does not exist, the use of this or that type of therapy depends on the location of the hemangioma, its size and response to therapy.

Aim: To attract the attention of pediatricians to the diagnosis of rare hematological syndromes.

Materials and methods. An extended examination of the child and a thorough differential diagnosis with other vascular anomalies has been performed.

Results. Based on the evaluation of history, clinical examination and laboratory and instrumental methods of examination, a diagnosis of Kazabah—Merritt syndrome was made.

Conclusions. The diagnosis of Kazabah—Merritt syndrome requires an extended examination of the child and careful differentiation with other vascular anomalies.

Key words: hemangiomas, thrombocytopenia, consumptive coagulopathy, children.

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Article received: May 07, 2018. Accepted for publication: Oct 29, 2018.